{"created":"2023-06-19T11:20:45.556036+00:00","id":836,"links":{},"metadata":{"_buckets":{"deposit":"42b92221-fdfd-4fc6-8c1c-ea0bac2f7507"},"_deposit":{"created_by":3,"id":"836","owners":[3],"pid":{"revision_id":0,"type":"depid","value":"836"},"status":"published"},"_oai":{"id":"oai:asahikawa-med.repo.nii.ac.jp:00000836","sets":["7","7:23"]},"author_link":["2486","2487","2488","2489","2490","2491","2492","2493","2494","2495"],"item_5_biblio_info_21":{"attribute_name":"書誌情報","attribute_value_mlt":[{"bibliographicIssueDates":{"bibliographicIssueDate":"2007-01-01","bibliographicIssueDateType":"Issued"},"bibliographicIssueNumber":"10","bibliographicPageEnd":"2004","bibliographicPageStart":"2003","bibliographicVolumeNumber":"28","bibliographic_titles":[{"bibliographic_title":"Therapeutic Research"}]}]},"item_5_description_33":{"attribute_name":"抄録","attribute_value_mlt":[{"subitem_description":"Bosentanを導入した膠原病性肺高血圧症患者6例の経過を報告した。投与4週間後、右室駆出率(RVEF)と右室重量は有意に改善し、BNP、心臓超音波所見によるTr△Pは低下傾向を示した。6分間歩行検査では自覚症状の改善と歩行距離の延長を認めた。12?18週では、BNPとTr△Pは更に低下し、RVEFも悪化しなかった。その後1例は死亡したが、6?22ヵ月内服継続中の5例(女・49?61歳)では、投与量は1例が125mg/日、4例が250mg/日で、BNPの再上昇を来たしたのは2例のみであった。Tr△Pの再上昇はなく、全例肺高血圧症はコントロールされていた。しかし原疾患の増悪に伴って間質性肺炎2例、腎機能障害1例の進行を認めた。死亡例はシェーグレン症候群患者で、bosentan投与後に肝機能障害が出現し、投与を中止してプレドニン・エポプレステノールを併用したが、アスペルギルス・サイトメガロウイルスの複合感染を発症し投与開始6ヵ月後に死亡した","subitem_description_language":"ja","subitem_description_type":"Abstract"}]},"item_5_description_36":{"attribute_name":"注記","attribute_value_mlt":[{"subitem_description":"著者版","subitem_description_type":"Other"}]},"item_5_description_37":{"attribute_name":"資源タイプ","attribute_value_mlt":[{"subitem_description":"text","subitem_description_type":"Other"}]},"item_5_description_41":{"attribute_name":"フォーマット","attribute_value_mlt":[{"subitem_description":"application/pdf","subitem_description_type":"Other"}]},"item_5_source_id_22":{"attribute_name":"ISSN","attribute_value_mlt":[{"subitem_source_identifier":"0289-8020","subitem_source_identifier_type":"PISSN"}]},"item_5_text_44":{"attribute_name":"ID(XooNIps)","attribute_value_mlt":[{"subitem_text_value":"2008115839"}]},"item_5_text_54":{"attribute_name":"閲覧数(XooNIps)","attribute_value_mlt":[{"subitem_text_value":"1247"}]},"item_5_text_55":{"attribute_name":"ダウンロード数(XooNIps)","attribute_value_mlt":[{"subitem_text_value":"941"}]},"item_5_text_7":{"attribute_name":"著者 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